The Human OXPHOS System -- Molecular Biology of the OXPHOS System -- Clinical Diagnosis of Oxidative Phosphorylation Disorders -- Contribution of Histopathological Examination to the Diagnosis of OXPHOS Disorders -- Biochemical Diagnosis of OXPHOS Disorders -- Mitochondrial DNA and OXPHOS Disorders -- Nuclear DNA and Oxidative Phosphorylation -- Cell Biological Consequences of OXPHOS Disorders …